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Case Reports (Online only) Autumn 2010, Volume 18 Issue 3: e 41-e 43

Invasive squamous cell carcinoma of the hand in a patient with Kindler syndrome: Case report and literature review

E Cardin-Langlois | D Hanna | M St-Amant | F Croteau

Kindler syndrome is a rare, autosomal, recessive genodermatosis characterized by trauma-induced acral blisters in infancy and childhood, photosensitivity and progressive poikiloderma. Very few cases in the literature report an association with squamous cell carcinoma, even though it is a very well-known, long-term complication. A case involving a 23-year-old woman with a history of Kindler syndrome who was admitted to the department of plastic surgery (Sherbrooke University, Sherbrooke, Quebec) with an extensive ulcerated squamous cell carcinoma of the right hand is presented. A local excision of the tumour was initially performed, but positive margins and clinically palpable axillary lymphadenopathy over the course of hospitalization necessitated below-elbow amputation and lymph node dissection. To the authors’ knowledge, this is the second reported case of aggressive metastatic squamous cell carcinoma of the hand in a patient with Kindler syndrome.

Aggressive squamous cell carcinoma | Bullous epidermolysis | Kindler syndrome | Photosensitivity | Poikilodermia
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